Congenital Absence of Left Pulmonary Artery with Coarctation of Right Pulmonary Artery.

Congenital unilateral absence of a pulmonary artery is a rare condition. Pool, Vogel, and Blount (1962), in a review of the English published material, collected 98 cases and described 4 of their own. Of this group 23 were proven examples of absence of the left pulmonary artery. Oakley, Glick, and McCredie (1963) described a further case, and Sherrick, Kincaid, and DuShane (1962) encountered 8 examples. This condition is uncommon as an isolated anomaly, and is most frequently seen in conjunction with the tetralogy of Fallot, but may also be associated with atrial and ventricular septal defects, and less commonly with patent ductus arteriosus. Apparently unilateral absence of the left pulmonary artery has not been reported in association with a coarctation of the right pulmonary artery.